HRCT-assessed fibrosis burden predicts mortality better than pulmonary function decline in progressive pulmonary fibrosis
BACKGROUND AND AIM: Progressive pulmonary fibrosis (PPF) is a clinically significant phenotype observed across fibrotic interstitial lung diseases (ILDs), characterized by pulmonary functional decline, radiologic progression, and worsening symptoms. While declines in forced vital capacity (FVC) and diffusing capacity f...