Sep 2026· International Journal of Innovative Technologies in Social Science· Vol 3· 0 citations· 15 references
TL;DR
A persistent gap exists between guideline recommendations and real-world management of FH, and improving early detection through enhanced use of genetic testing, optimization of cascade screening, and timely initiation of lipid-lowering therapy may reduce cumulative LDL-C exposure and improve long-term cardiovascular outcomes.
Abstract
Background. Familial hypercholesterolemia (FH) is a common autosomal dominant genetic disorder associated with premature atherosclerotic cardiovascular disease. Despite established international guidelines, FH remains substantially underdiagnosed, particularly in young adults.
Aim. This narrative review summarizes current evidence on diagnostic challenges and barriers to guideline implementation in this population.
Methods. A narrative literature review was conducted using PubMed/MEDLINE, Scopus, and Web of Science databases. The review focused on evidence regarding FH epidemiology, diagnostic approaches, genetic testing, cascade screening, treatment strategies, and implementation gaps in young adults.
Results. Registry data indicate that the median age of FH diagnosis is 44.4 years, suggesting delayed identification and prolonged exposure to elevated low-density lipoprotein cholesterol levels during early adulthood. In young adults, diagnosis is often limited by the absence of overt clinical signs, reducing the utility of clinical scoring systems such as the Dutch Lipid Clinic Network criteria. As a result, diagnosis relies primarily on lipid measurements, family history, and genetic testing. However, genetic testing and cascade screening remain underutilized in routine clinical practice.
Conclusions. A persistent gap exists between guideline recommendations and real-world management of FH. Delayed diagnosis and suboptimal implementation of treatment strategies contribute to inadequate cardiovascular risk reduction in young adults. Improving early detection through enhanced use of genetic testing, optimization of cascade screening, and timely initiation of lipid-lowering therapy may reduce cumulative LDL-C exposure and improve long-term cardiovascular outcomes.
The findings support the clinical value of genetic testing in familial hypercholesterolemia, both for improving diagnostic accuracy and for promoting earlier therapeutic intervention and adherence.
Daniele Perrino, Delia Monopoli, D. Verrigni et al.· European Journal of Pediatri...· 0 citations
Evidence suggests that earlier diagnosis and or treatment of FH, as a proxy for screening evidence, is associated with improved surrogate outcomes in children and cardiovascular outcomes in adults.
VC Umeokwoaka, L. Comber, OM Jenkins et al.· European Journal of Public H...· 0 citations
Introduction: Homozygous familial hypercholesterolemia (HoFH) is a rare but severe genetic disorder characterized by extremely elevated LDL-C levels from birth, leading to accelerated atherosclerosis and premature cardiovascular disease. Despite advances in lipid-lowering therapies, the evidence guiding clinical practi...
Álvaro J. Ruiz, Rafael Campo-Torrenegra, Claudia Monsalve-Arango et al.· Revista Colombiana de Endocr...· 0 citations
ABSTRACT Introduction Familial hypercholesterolemia (FH) is an autosomal dominant disorder characterized by raised levels of low-density lipoprotein cholesterol (LDL-C) and premature cardiovascular disease (CVD), with a prevalence of 1 in 300, which can be successfully treated. These features make it amenable for large...
A. Wierzbicki· Expert Review of Cardiovascu...· 0 citations
Abstract Familial hypercholesterolemia (FH) is a common genetic disorder causing elevated low-density lipoprotein cholesterol (LDL-c) concentrations from birth, resulting in a high risk of premature cardiovascular disease. Despite effective early treatment, FH remains underdiagnosed in children, highlighting the need f...
Vera H. de Kleijne, B. Hutten, A. Boelen et al.· Clinical Chemistry and Labor...· 0 citations
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